Volume 2, Issue 1, January 2014, Page: 1-4
A Robust Allegation of Von Hippel-Lindau (VHL) Associated Hemangioblastoma in the Central Nervous System (CNS): A Case Report
Muhammad Yunus Amran, Hasanuddin University Teaching Hospital, Department of Neurology, Faculty of Medicine, Hasanuddin University, Makassar, South Sulawesi, Indonesia
Hasmawaty Basir, Hasanuddin University Teaching Hospital, Department of Neurology, Faculty of Medicine, Hasanuddin University, Makassar, South Sulawesi, Indonesia
Andi Kurnia Bintang, Hasanuddin University Teaching Hospital, Department of Neurology, Faculty of Medicine, Hasanuddin University, Makassar, South Sulawesi, Indonesia
Muhammad Akbar, Hasanuddin University Teaching Hospital, Department of Neurology, Faculty of Medicine, Hasanuddin University, Makassar, South Sulawesi, Indonesia
Received: Oct. 22, 2013;       Published: Jan. 10, 2014
DOI: 10.11648/j.ijmi.20140201.11      View  2508      Downloads  107
Abstract
Haemangioblastoma, a benign vascular tumor derived from the capillary of endothelial cells, is an inherited disorder due to an autosomal dominant trait. The prevalence rates accounted for 1% to 2.5% of all intracranial tumors and 2% to 3% of all intramedullary spinal cord tumors. We report the infrequent case of a robust allegation of von Hippel-Lindau (VHL) associated haemangioblastoma in the central nervous system of a man. A 20 years old male presented to the hospital with the chief complaint of progressive chronic cephalgia three months prior to hospitalization. He complained also of blurred vision on neurologic examination; there is papilla edema with suspicion of retinal edema. Radiological examination result suggested a cerebellar haemangioblastoma dextra with noncommunicating hydrocephalus. After the first operation (installation of VP shunting) and subsequent operation (excision of the tumor), the pathological anatomy results revealed a cavernous angioma.
Keywords
Haemangioblastoma, CNS, CT-Scan, Von Hippel-Lindau Diseases
To cite this article
Muhammad Yunus Amran, Hasmawaty Basir, Andi Kurnia Bintang, Muhammad Akbar, A Robust Allegation of Von Hippel-Lindau (VHL) Associated Hemangioblastoma in the Central Nervous System (CNS): A Case Report, International Journal of Medical Imaging. Vol. 2, No. 1, 2014, pp. 1-4. doi: 10.11648/j.ijmi.20140201.11
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